A CASE OF LYMPHANGIOLEIOMYOMATOSIS WITH MULTIPLE ANGIOMYOLIPOMAS IN THE KIDNEYS: A CASE REPORT

Authors

  • How SH
  • Azlin S
  • Pang YK
  • Liam CK

Abstract

Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and
blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat.

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Published

2006-12-26

Issue

Vol. 9 No. 2 (2006)

Section

Research article

License

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